Gastrointestinal Erdheim-Chester disease.
نویسندگان
چکیده
We report a rare case of Erdheim-Chester Disease, a non-Langerhans cell histiocytosis. A 60-year old female presented with a seven-month history of vague abdominal symptoms. A large retroperitoneal mass was detected on computed tomography (CT), but multiple CT-guided biopsy samples were inconclusive. Laparoscopy revealed a mass in the distal ileum, which was resected. Histology and immuno-histochemistry supported a diagnosis of Erdheim-Chester Disease.
منابع مشابه
Multisystem Radiologic Manifestations of Erdheim-Chester Disease
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ورودعنوان ژورنال:
- Irish medical journal
دوره 107 5 شماره
صفحات -
تاریخ انتشار 2014